Diffusion Tensor MR Imaging in Children with Pantothenate Kinase−Associated Neurodegeneration with Brain Iron Accumulation and Their Siblings
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چکیده
منابع مشابه
Diffusion tensor MR imaging in children with pantothenate kinase-associated neurodegeneration with brain iron accumulation and their siblings.
BACKGROUND AND PURPOSE It has been reported that iron concentration influences DTI metrics in deep gray matter nuclei. We hypothesized that increased FA in the deep gray nuclei may indicate abnormal iron accumulation in patients with PKAN and their siblings. MATERIALS AND METHODS Seven patients with the characteristic "eye-of-the-tiger sign," their 5 siblings, and 5 age-matched controls were ...
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ژورنال
عنوان ژورنال: American Journal of Neuroradiology
سال: 2009
ISSN: 0195-6108,1936-959X
DOI: 10.3174/ajnr.a1849